phenylalanine hydroxylase

听听怎么读
[ˌfenəlˈæləni:n haiˈdrɔksileis]
是什么意思
  • 释义

    [医]苯丙氨酸羟化酶;

  • 英英释义

    Phenylalanine hydroxylase

    • Phenylalanine hydroxylase (PheOH, alternatively PheH or PAH) () is an enzyme that catalyzes the hydroxylation of the aromatic side-chain of phenylalanine to generate tyrosine. PheOH is one of three members of the pterin-dependent amino acid hydroxylases, a class of monooxygenase that uses tetrahydrobiopterin (BH4, a pteridine cofactor) and a non-heme iron for catalysis.

    以上来源于:Wikipedia

    学习怎么用

    权威例句

    Hyperphenylalaninemia: Phenylalanine Hydroxylase Deficiency
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    Cloned human phenylalanine hydroxylase gene allows prenatal diagnosis and carrier detection of classical phenylketonuria.
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    Molecular genetics of tetrahydrobiopterin-responsive phenylalanine hydroxylase deficiency †
    Mutational spectrum of phenylalanine hydroxylase deficiency in Sicily: implications for diagnosis of hyperphenylalaninemia in southe...
    Crystal structure of the catalytic domain of human phenylalanine hydroxylase reveals the structural basis for phenylketonuria
    Nucleotide sequence of a full-length complementary DNA clone and amino acid sequence of human phenylalanine hydroxylase.
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